Two Cases of Chronic Idiopathic Ataxic Sensory Neuropathy

J Korean Neurol Assoc > Volume 10(2); 1992 > Article

Journal of the Korean Neurological Association 1992;10(2): 209-218.

만성 원발성 운동실조성 감각신경병증 2례

문준식, 박영관,선우일남,김기환,김장성,지제근

연세대학교 신경과. 인제대학교 신경과. 서울대학교 병리학.

Two Cases of Chronic Idiopathic Ataxic Sensory Neuropathy

Joon-Shik Moon, M.D., Young-Gwan Park, M.D., Il-Nam Sunwoo, M.D., Ki-Whan Kim, M.D., Jang-Sung Kim, M.D., Je-Geun Ii, M.D.

Department of Neurology, College of Medicine, Yoensei University. Department of Neurology, College of Medicine, Inje University, Department of Pathology, College of Medicine, Seoul National University

Abstract

Sensory neuropathy is characterized by pure sensory dysfunction, ultimately evolving into areflexia and severe sensory ataxia in spite of the preservation of the other functions in the nervous system such as motor function. This disorder is known to be commonly found in cancer patients as a paraneoplastic syndrome, but nowadays many reports are made that sensory neuropathy is not merely related to malignancy but also with autoimmune disorders such as Sjogren's syndrome or polyclonal gammopathy, etc. Hence we report two patients who have been diagnosed as chronic idiopathic ataxic sensory neuropathy through electrophysiological and histopathological studies without any evidence of cancer or any other known cause.