A Case of Multifocal Fibrosclerosis with CNS Involvement

J Korean Neurol Assoc > Volume 8(2); 1990 > Article

Journal of the Korean Neurological Association 1990;8(2): 372-377.

중후신경계를 침범한 다발성 섬유경화증 1예

이계훈, 차재관, 김주한 , 정경천, 이종철

한양대학교 신경과, 내과.

A Case of Multifocal Fibrosclerosis with CNS Involvement

Kye Hoon Lee, M.D., Jae Kwan Cha, M.D., Ju Han Kim, M.D., Kyung Cheon Chung, M.D. Jong Cheol Rhee, M.D.*

Dep. Of Neurology & Internal Medicine*, Hanyang University

Abstract

Multifocal fibrosclerosis, a rare disorder, has no known etiology and is considered to be a systemic illness manifested by combinations of fibrosing process of multiple areas such as mediastinal fibrosis, retroperitoneal fibrosis, orbital pseudotumor, sclerosing cholangitis, and Reidel's thyroiditis. We have experienced a 49-year-old man with pseudotumor of the orbit, sclerosing cholangitis, and CNS involvements included unrecognized meningitis and suspicious CNS vasculitis. The patient showed clinical improvement with corticosteroid therapy.