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J Korean Neurol Assoc. 2007;25(1):101-104.
- Acquired Hepatocerebral Degeneration Presenting with Downbeat Nystagmus and Ataxia: A Case Report
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Chang-Min Lee
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Department of Neurology, Dankook University College of Medicine, Cheonan, Korea
- 하향안진과 운동실조를 보인 후천성 간뇌변성
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이창민, 유호준 유정암 김재일
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단국대학교 의과대학 신경과학교실
- Abstract
- Nystagmus or ataxia is a rare manifestation of acquired hepatocerebral degeneration (AHCD). A 49-year-old woman presented with downbeat nystagmus and limb and gait ataxia. She was diagnosed as primary biliary cirrhosis with a gastric varix. Brain MRI showed cerebellar vermian atrophy and characteristic T1 high-signal intensities in bilateral globus pallidi and ventral midbrain. We report a rare case of AHCD manifesting prominent cerebellar symptoms. This has not yet been reported in Korea.KeyWords:Acquired hepatocerebral degeneration, Downbeat nystagmus, Ataxia
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