- J Korean Neurol Assoc. 2002;20(5):568-570.
- Two Cases of Evans Myopathy in a Family
- Jung Hee Cho, M.D.
- Departments of Neurology, Yonsei University College of Medicine
- 한 가족에서 발병한 Evans 근병증 2예
- 조정희 , 정연경 ·김승민 ·선우일남
- 연세대학교 의과대학 신경과
- Abstract
- "Evans myopathy is a type of malignant hyperthermia showing characteristic distribution of myopathic changes. We
present two cases of Evans myopathy, father and his son in a family. Five members of this family expired during anes-thesia
and surgery and two of these cases were reported as the malignant hyperthermia. The muscle pathology shows
moth-eaten appearance with or without unstained cores in NADH-TR stain and its difference between the father and his
son is suggestive of rather progressive myopathy than static one.Key Words : Evans myopathy, Malignant hyperthermia"
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