Korean Journal of Sport Science

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J Korean Neurol Assoc. 2001;19(5):544-546.
A Case of Kennedy Syndrome Mimicking Myasthenia Gravis
"Byung-Ju Lee, M.D., Ki-Han Kwon, M.D., Sung-Min Kim, M.D., Ha-ry Na, M.D., Byung-Chul Lee, M.D., Sang-Hyo Ryu,M.D., Jae-Chun Bae, M.D., Jee-In Kim.*, Jin-Sung Lee, M.D. †"
"Department of Neurology, Hallym University College of Medicine Division of Genetic Disease, National Institute of Health, Korea* Department of Pediatrics, Yonsei University College of Medicine †"
중증근무력증과 유사한 구척수 근위축증(Kennedy 증후군)1예
이병주, "권기한.김성민나해리이병철류상효배재천김지인*이이진성 †"
한림대학교 의과대학 신경과학교실,국립보건원 유전질환과*,연세의대 소아과학교실
Abstract
"Patients with Kennedy syndrome, which progresses more slowly than amyotrophic lateral sclerosis show a mild degree of motor fluctuation but rarely show significant decremental responses to repetitive nerve stimulations. Even in a patient with decremental responses to repetitive nerve stimulations, there is usually no significant improvements in motor symptoms to anticholinesterases. We experienced a patient with Kennedy syndrome, who showed significant decremental responses to repetitive nerve stimulations and a marked degree of motor fluctuation. His motor fluctuation responded dramatically to anticholinesterase. J Korean Neurol Assoc 19(5):544~546, 2001 Key Words : Kennedy syndrome, Decremental response, Anticholinesterase"

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