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J Korean Neurol Assoc. 1998;16(2):241-244.
- A Case of Porphyria with reversible MRI findings
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Suk-Yun Kang, M.D., Hyeo-Il Ma, M.D., Kyu-Hwan Kwak, M.D., San-Ahm Lee, M.D.
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Dept. of Neurology, Ulsan University, College of Medicine, Asan Medical Center
- 포르피린증 환자에서 보인 가역적 자기공명영상소견 1례
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강석윤, 마효일 , 곽규환 , 이상암
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울산대학교 의과대학 서울중앙병원 신경과학교실
- Abstract
- The porphyrias are inherited or acquired disorders of specific enzymes in the heme biosynthetic pathway. Porphyrias have diverse neurologic manifestations with unknown mechanism. Some authors have proposed ischemic vasculopathy as a cause of neurologic deficits, which was supported by reversible MRI lesions in porphyrias. We report a rare case with reversible MRI findings in porphyria. A 27-year-old woman was presented with seizures and hallucinations. MRI revealed multiple lesions of both hemispheres. After treatment, MRI lesions showed marked resolution of signal abnormalities.
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