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J Korean Neurol Assoc. 1990;8(2):344-348.
- A Case of Hereditary Progressive Dystonia With Diurnal Fluctuation
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Dong Hun Kim, M.D., Sang Ok Ra, M.D., Seon Chool Hwang, M.D., Mun Sung Choi, M.D. Kyu Hyun Park, M.D.*, Sang Wook Kim, M.D.*, Dae Soo Jung,
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Dep. Of Neurology, Maryknoll Hospital
- 증상의 일중 변화를 보이는 Hereditary Progressive Dystonia 1 예
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김동훈, 나상옥,황선출,최문성,박규현,김상욱,정대수
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메리놀병원 신경과. 부산대학교 신경과. 춘해병원 신경과.
- Abstract
- Hereditary progressive dystonia develope in the first decade of ?life and is characterized by marked
diurnal fluctuation of symptoms(dystonic postures and movements),? i.e.symptoms aggrevated towards
evening and alleviated after sleep.
These symptoms and signs responded dramatically to levodopa. ?With the high incidence of familial
cases this disorder is considers to be hereditary, but ?inheritance is not clear yet. Segawa regarded this
disorder as a dystonia different from Parkinson's disease and ?other types of dystonic movement
disorders, thereafter it has been reported under name of ?hereditary progressive dystonia with marked
diurnal fluctuation.
Keywords :
- 초록
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