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J Korean Neurol Assoc. 1985;3(2):2091-297.
- A Cases of Familial Spastic Paraplegia (FSP)
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Jung-Sang Ha,M.D.,Won-Hee Choi, M.D., Choong-Seo Park, M.D., Yung-Joo Byun, M.D., Bo-Wan Seo, M.D.
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Department of Neurology, Pathology, Yungnam University
- 가족성 경성 대마비 1례
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하정상, 서보완, 변영주, 박충서, 최원희
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영남대학교 신경과, 해부병리학.
- Abstract
- We present a family of FSP with review of literatures.
Seeligmuller (1876) and Strumpell (1880) were the first to describe familial case of
spastic paraplegia characterized by progressive weakness and spasticity of the lower limbs
with little or no involvement of the upper extremities.
This syndrome is heterogenous in inheritance, age of onset, severity and associated
signs.
A pure type without complications has been named ""Strumpell's FSP.""
We have recently experienced a case of 17 years old male who had bilateral weakness
and stiffness of lower extremities, and gait disturbance with family history.
Differential diagnosis, particularly with familial amyotrophic lateral sclerosis, is discussed.
Keywords :
- 초록
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